Overview
Status dystonicus is a rare, but life-threatening movement disorder emergency. Paroxysmal auto- nomic instability with dystonia (PAID) is increasingly recognized in children. Urgent assessment is required, and management is tailored to patient characteristics and complications.
Most Recent References
Pallidal deep brain stimulation in a 5-year-old child with dystonic storm: case report. Aydin S, Abuzayed B, Uysal S, et al. Turk Neurosurg 2013; 23: 125–8
Status dystonicus: a practice guide. Allen NM, Lin JP, Lynch T, King MD. Dev Med Child Neurol. 2014 Feb;56(2):105-12.
Status dystonicus: predictors of outcome and progression patterns of underlying disease. Fasano A, Ricciardi L, Bentivoglio AR, et al. Mov Disord 2012; 27: 783–8.